Odontogenic fibromyxoma is a benign odontogenic mesenchymal tumor of the jaws. It affects people in the second to the fourth decade of life with a female predominance. Jaws are rarely involved by this lesion with a mandible predilection. This tumor represents a subgroup of myxoma which are characterized by primitive mesenchymal cells proliferation producing an amorphous mucoid-rich intercellular matrix. The collagen fiber content is higher in the case of fibromyxoma, hence his name. This odontogenic lesion is subdivided into central fibromyxoma and peripheral one. The intraosseous type is more common and easier to diagnose, however, the extraosseous variety is extremely rare and presents always a diagnostic challenge. That’s motivate this work which aimed to report a case of a peripheral fibromyxoma involving the right maxilla diagnosed in an adult male patient, in order to highlights the clinical and histological features of this tumor, propose the diagnostic approach, detail the treatment option and the follow up procedures.